Oral Surg Oral Med Oral Pathol. Dec;68(6) Familial gigantiform cementoma: classification and presentation of a large pedigree. Young SK(1). Gigantiform cementoma is a rare, benign fibro-cemento-osseous disease of the jaws, seen most frequently in young girls. Radiographically, it typically presents. PDF | Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Undocumented.
|Published (Last):||2 December 2010|
|PDF File Size:||19.35 Mb|
|ePub File Size:||15.70 Mb|
|Price:||Free* [*Free Regsitration Required]|
The disorder appears to occur mainly in asymptomatic black females with a mean age of onset of 42 years. Besides, his pelvis was also considered to be susceptible to fractures because both cortical and trabecular bones were undergoing a cemengoma or osteopenic conversion signifying an unexpected calcium loss.
Microscopic examination showed a lobular calcified cementpma with a peripheral zone of fibropsammomatous tissue corresponding with the radiolucent margin. Familial florid cemento-osseous dysplasia — a case report and review of the literature.
Familial gigantiform cementoma with brittle bone disease, pathologic fractures, and osteosarcoma: Micrograph demonstrating the bony mass showing a lobular appearance with small marrow spaces arrows. According to the World Health Organization classification of osseous dysplasias ODFGC is generally regarded as an odontogenic lesion that shares a same periodontal ligament origin with focal, periapical. Surgical removal of the affected bone is needed, and has to be followed by reconstruction.
Unsourced material may be challenged and removed. Focal OD is a solitary lesion affecting a single area in the jaw bone and mainly the posterior quadrant of the jaws. A The adolescent patient’s aunt who had received surgery nonvascularized iliac bone reconstruction 30 years ago now complaint of anterior maxillary mass with cementima infection.
A radiolucent margin is present around most of the lesion. Benign fibro-osseous diseases of the maxillofacial bones.
Please help improve this article by adding citations to reliable sources. A provisional diagnosis of an osteoma was made and the lesion was enucleated through the buccal cortical plate. Cemento-osseous dysplasia of the jaw bones: Apart from typical multiquadrant and expansile abnormalies involving both jaws, he also suffered from several times of fractures in lower extremity.
We present an adolescent case with recurrent cemebtoma gigantiform cementoma who received surgical intervention in our hospital. B Reconstructed computed tomography image of familial gigantiform cementoma appearance.
Gigantiform cementoma – Wikipedia
D Postoperative view of patient after bilateral mandibulectomy. Macroscopic features of the enucleated specimen.
Furthermore, radiographic examinations of calvaria, pelvis, femoris, tibia, and fibula all revealed radiolucent areas signifying diffuse osteopenic bone losses. S50—S70 [ PubMed ]. National Center gigantifor Biotechnology InformationU.
This is an open access article distributed under the Cementomw Commons Attribution License 4. Therefore, we present a case with a large FGC family history so as to sketch a more detailed portrait of such ailment. Discussion Osseous dysplasias ODs are generally slow growing, non-expansive, fibro-osseous jaw lesions of unknown aetiology. The cause of this tumor is currently unknown.
Although our patient is young, the absence of a family history does not fulfill the qualification for the diagnosis of a FGC type of OD.
There was a problem providing the content you requested
Case report A 6-year-old female presented with a main complaint of a painless maxillary swelling which her parents noticed 8 months earlier. Abstract The objective of this report is to present an unusual case of a gigantiform cementoma manifesting with gross expansion of the maxilla in a 6-year-old black female. The feasibility of using fibular flaps was ruled out in view of his unfortunate history of frequent lower-extremity fractures.
Radiographs of fracture areas in 1 patient showed osteopenic bone and excess callus formation. OMIM is intended for use primarily by physicians and other professionals concerned with genetic disorders, by genetics researchers, and by advanced students in science and medicine. This page was last edited on 11 Octoberat A review of latest gigsntiform showed that mandible remains to be the most seriously affected organ, in contrast to maxillary lesion.
Open in a separate window.
Incomplete removal or shave-off contouring are ill advised, as the lesions enlarge more rapidly tigantiform the early radiolucent stage. Author information Article notes Copyright and License information Disclaimer.